Clinical aspects, neuroimaging and electrophysiological behavior of hydranencephaly

Abstract

There is a big similarity between hydranencephaly and severe congenital hydrocephalus clinically as well as in image studies. Generally the electroencephalogram does not show electrical activity and the brain stem auditory evoked potentials are normal. This article presents four cases of children with hydranencephaly associated to bilateral carotid occlusion and clinical neuroimage aspects as well as brainstem auditory potentials, sleep profile, epilepsy and subclinical epileptiform EEG activity are discussed.